Arrhythmogenic right ventricular cardiomyopathy (ARVC) causes ventricular arrhythmias (VAs) and sudden cardiac death (SCD). In 2019, a risk prediction model that estimates the 5-year risk of incident VAs in ARVC was developed (ARVCrisk.com). This study aimed to externally validate this prediction model in a large international multicentre cohort and to compare its performance with the risk factor approach recommended for implantable cardioverter-defibrillator (ICD) use by published guidelines and expert consensus.

Arrhythmic risk prediction in arrhythmogenic right ventricular cardiomyopathy: external validation of the arrhythmogenic right ventricular cardiomyopathy risk calculator / Jordà, Paloma; Bosman, Laurens P; Gasperetti, Alessio; Mazzanti, Andrea; Gourraud, Jean Baptiste; Davies, Brianna; Frederiksen, Tanja Charlotte; Moreno Weidmann, Zoraida; Di Marco, Andrea; Roberts, Jason D; Macintyre, Ciorsti; Seifer, Colette; Delinière, Antoine; Alqarawi, Wael; Kukavica, Deni; Minois, Damien; Trancuccio, Alessandro; Arnaud, Marine; Targetti, Mattia; Martino, Annamaria; Oliviero, Giada; Pipilas, Daniel C; Carbucicchio, Corrado; Compagnucci, Paolo; Dello Russo, Antonio; Olivotto, Iacopo; Calò, Leonardo; Lubitz, Steven A; Cutler, Michael J; Chevalier, Philippe; Arbelo, Elena; Priori, Silvia Giuliana; Healey, Jeffrey S; Calkins, Hugh; Casella, Michela; Jensen, Henrik Kjærulf; Tondo, Claudio; Tadros, Rafik; James, Cynthia A; Krahn, Andrew D; Cadrin-Tourigny, Julia. - In: EUROPEAN HEART JOURNAL. - ISSN 0195-668X. - (2022). [10.1093/eurheartj/ehac289]

Arrhythmic risk prediction in arrhythmogenic right ventricular cardiomyopathy: external validation of the arrhythmogenic right ventricular cardiomyopathy risk calculator

Compagnucci, Paolo;Dello Russo, Antonio;Casella, Michela;
2022-01-01

Abstract

Arrhythmogenic right ventricular cardiomyopathy (ARVC) causes ventricular arrhythmias (VAs) and sudden cardiac death (SCD). In 2019, a risk prediction model that estimates the 5-year risk of incident VAs in ARVC was developed (ARVCrisk.com). This study aimed to externally validate this prediction model in a large international multicentre cohort and to compare its performance with the risk factor approach recommended for implantable cardioverter-defibrillator (ICD) use by published guidelines and expert consensus.
2022
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Utilizza questo identificativo per citare o creare un link a questo documento: https://hdl.handle.net/11566/305293
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