The development of renal cell carcinoma in Adult Polycystic Kidney Disease (APKD) has been reported in the literature; one of the features of renal malignancy in APKD is the difficulty to make a diagnosis, and the majority of cases reported are incidental findings at surgery or autopsy. We report a rare case of renal sarcoma in a patient with APKD. Sarcoma associated with APKD does not seem to have particular biological characteristics when compared with primary renal sarcoma; however the polycystic kidney represents an aggravating circumstance, because of the difficulty in making an early diagnosis of a disease with a poor prognosis.
Renal sarcoma associated with adult polycystic kidney disease. A case report and literature review / Minardi, Daniele; Mantovani, P.; Dellabella, M.; Dell'Atti, L.; Mazzucchelli, Roberta; Santinelli, Alfredo; Scarpelli, Marina; Muzzonigro, Giovanni. - In: ARCHIVIO ITALIANO DI UROLOGIA ANDROLOGIA. - ISSN 1124-3562. - STAMPA. - 76:2(2004), pp. 94-96.
Renal sarcoma associated with adult polycystic kidney disease. A case report and literature review.
MINARDI, Daniele;MAZZUCCHELLI, Roberta;SANTINELLI, ALFREDO;SCARPELLI, Marina;MUZZONIGRO, GIOVANNI
2004-01-01
Abstract
The development of renal cell carcinoma in Adult Polycystic Kidney Disease (APKD) has been reported in the literature; one of the features of renal malignancy in APKD is the difficulty to make a diagnosis, and the majority of cases reported are incidental findings at surgery or autopsy. We report a rare case of renal sarcoma in a patient with APKD. Sarcoma associated with APKD does not seem to have particular biological characteristics when compared with primary renal sarcoma; however the polycystic kidney represents an aggravating circumstance, because of the difficulty in making an early diagnosis of a disease with a poor prognosis.I documenti in IRIS sono protetti da copyright e tutti i diritti sono riservati, salvo diversa indicazione.
