Background: Perivascular epithelioid cell tumours (PEComas) represent a rare group of mesenchymal tumours with an unpredictable outcome. They are usually observed in middle-aged women whilst they are very rare in children, with limited cases described. Due to the rare anatomical location in kidneys, a correct diagnosis and treatment is really challenging. Methods: We observed and treated a case of kidney's PEComa in a 14-year-old boy. Results: An individualized approach based on anatomical (3D CT-reconstructions) and histopathological (US-guided preliminary biopsy) features lead us to perform a successful robotic-sparing surgery enabling the preservation of two-thirds of the kidney involved. Conclusions: A meticulous preoperative planning in selected patients can lead to a minimally invasive approach even in some paediatric kidney's neoplasms. © 2020 John Wiley & Sons Ltd.
Individualized robotic organ-sparing surgery in a paediatric case of renal perivascular epithelioid cell tumour / Silveri, M; Natali, Gl; Cobellis, G; Gregori, L; Torino, G. - In: THE INTERNATIONAL JOURNAL OF MEDICAL ROBOTICS AND COMPUTER ASSISTED SURGERY. - ISSN 1478-596X. - STAMPA. - 16:5(2020), pp. 1-4.
Individualized robotic organ-sparing surgery in a paediatric case of renal perivascular epithelioid cell tumour
Cobellis GMembro del Collaboration Group
;
2020-01-01
Abstract
Background: Perivascular epithelioid cell tumours (PEComas) represent a rare group of mesenchymal tumours with an unpredictable outcome. They are usually observed in middle-aged women whilst they are very rare in children, with limited cases described. Due to the rare anatomical location in kidneys, a correct diagnosis and treatment is really challenging. Methods: We observed and treated a case of kidney's PEComa in a 14-year-old boy. Results: An individualized approach based on anatomical (3D CT-reconstructions) and histopathological (US-guided preliminary biopsy) features lead us to perform a successful robotic-sparing surgery enabling the preservation of two-thirds of the kidney involved. Conclusions: A meticulous preoperative planning in selected patients can lead to a minimally invasive approach even in some paediatric kidney's neoplasms. © 2020 John Wiley & Sons Ltd.I documenti in IRIS sono protetti da copyright e tutti i diritti sono riservati, salvo diversa indicazione.
